Atypical Hemolytic Uremic Syndrome in Tertiary Hospital, Pakistan
نویسندگان
چکیده
Atypical hemolytic uremic syndrome (HUS) is a rare disorder in children, therefore it may lead to misdiagnosis, delay in treatment, or acute kidney injury. Patients with atypical HUS present signs and symptoms of hemolytic anemia, thrombocytopenia, and higher lactate dehydrogenase and uric acid levels. The main risk factor highlighted is consanguinity, gene mutations, and viral infections. Eculizmab, a humanized anti-C5 monoclonal antibody, has been shown to be an effective treatment modality for such patients. This article will discuss atypical hemolytic uremic syndrome, present case report of a patient suffering with atypical HUS with bad prognosis and poor recovery.
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Concurrent Atypical Hemolytic Uremic Syndrome and Autoimmune Hemolytic Anemia: a case report
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1Department of Pediatrics, Clinical Sciences Lund, Lund University, Lund, Sweden; 2Department of Biological Infection, Hans Knoell Institute for Natural Products Research, Jena, Germany; 3Department of Internal Medicine, Regional Hospital, Halmstad, Sweden; 4Department of Pediatric Nephrology, University of Texas Health Science Center at San Antonio, TX; 5Division of Renal Medicine, Karolinska ...
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